Endovascular stenting of chronic retrohepatic inferior vena cava interruption in Budd-Chiari syndrome.
Budd-Chiari syndrome is a rare cause of hepatic venous outflow obstruction, with heterogenous etiologies. We report the case of a 35-year-old man with chronic, compensated Budd-Chiari syndrome due to retrohepatic inferior vena cava (IVC) occlusion, likely resulting from early-life thrombosis. Imagin…
Ten-year spontaneous intracranial hypotension with acquired tonsillar descent and syringomyelia from a T3-4 ventral dural defect: importance of digital subtraction myelography localization and role of direct repair. Illustrative case.
Spontaneous intracranial hypotension (SIH) is an underrecognized yet increasingly diagnosed cause of orthostatic headaches. Reduction of intracranial CSF volume and pressure produces characteristic imaging findings such as diffuse pachymeningeal enhancement and cerebellar tonsillar descent, mimickin…
Cervicomedullary CSF space obliteration as a risk factor of reoperation in Chiari malformation type I.
In patients with Chiari malformation type 1 (CM1), it is unclear whether severe cervicomedullary CSF space crowding on preoperative MRI is associated with postoperative outcomes. We tested whether a binary classification scheme of cervicomedullary CSF space crowding (obliteration vs. non-obliteratio…
Neurocognitive and affective dysfunction in Chiari malformation type I.
Chiari malformation type I (CM-I) is traditionally conceptualized as a structural disorder of the posterior cranial fossa characterized by cerebellar tonsillar herniation. However, increasing clinical and experimental evidence suggests that CM-I may be associated with distributed neurocognitive and…
"Intrapericardial Approach" for Venous Outflow Reconstruction in Living-Donor Liver Transplantation for Budd-Chiari Syndrome: Surgical Techniques and LongTerm Outcomes.
Unlike deceased-donor liver transplantation, living-donor liver transplantation (LDLT) for Budd-Chiari Syndrome (BCS) presents distinctive challenges in hepatic venous (HV)-outflow reconstruction because diseased HV-inferior vena cava (IVC) cannot be entirely replaced with healthy donor vessels. In…
Budd-Chiari Syndrome Due to Protein C Deficiency: A Case Report.
Budd-Chiari Syndrome (BCS), a rare vascular disorder of the liver characterized by obstruction of hepatic venous outflow, has an estimated prevalence of approximately 1 in 100,000 in the general population. Among its various etiologies, coagulation factor deficiencies are uncommon. This case, follow…
Not all acute peripheral facial palsy in children recovers completely: A telediagnostic follow-up study.
Up to 30% of adults with peripheral facial palsy (FP) develop synkinesis, but it's incidence in children remains unclear due to limited long-term data. Children (<18 years) treated for acute peripheral FP at Jena University Hospital between 2009 and 2021 were screened in this cross-sectional study.…
Pregnancy After In Vitro Fertilization in Budd-Chiari Syndrome Secondary to Polycythemia Vera: Multidisciplinary Management and Perioperative Considerations.
Budd-Chiari syndrome (BCS) is a rare hepatic vascular disorder frequently associated with prothrombotic conditions such as myeloproliferative neoplasms. Pregnancy and assisted reproductive technologies further increase thrombotic and portal-hypertensive risk. We report a successful in vitro fertiliz…